In the beginning what is thalassemia
thalassemia syndromes defined as group of usually inherited chronic disorder characterized by an absence or decreases synthesis of one the normal globin chains of hemoglobin
thalassemia consists of two types which are caused by a decrease in alpha and beta chain
type 1 thalassemia minor
type B thalassemia major
Nursing care plane and intervention for thalassemia
Anxiety and fear related to diagnostic procedure and blood transfusion
Nursing Goal :
The child family will become knowledgeable about the disease
Nursing intervention :
1- Explain the procedure not only for family but also to child.
2- explain the important of blood transfusion .
3- Remain with the child during tests and during blood transfusion .
The child and family have minimal anxiety ad\ns understand of disease and treatment
Management of therapeutic regimen individual effectively
Nursing Goal : The child will take his therapeutic effectively
Nursing intervention :
1- The nurse must administer transfusion therapy
2- the nurse administer chelation therapy
3- teach child and his parents the usage of chelation therapy and its side effect which always be abdominal discomfort and mild diarrhea
4- Give adequate amount of vitamin C but give it not at mealtime because vitamin c increase absorption of iron
The child receive his therapeutic management effectively.
3- Nursing diagnosis
Risk of infection due to anemia
Nursing goal : The child will have no signs of infection.
Nursing Intervention :
The nurse must do the following
1-Isolate the child from all known sources of infection.
2- Monitor the child temperature every 4 hours , because elevate in temperature indicates infection.
3- Administer antibiotic as the physician order as prophylactic measure.
4-give patient high protein diet in small meal .
5- if he didn't received vaccines at younger administer vaccine especially Hemophilus b polysaccharide vaccine at age 18 months .
4- Nursing diagnosis
Knowledge deficit related to disease and chelation therapy .
Nursing goal : Parents will verbalize an understanding of home care.
Nursing intervention : The nurse instruct and teach the parents about the following
1- Signs and symptoms of the disease .
2- how to administration of the chelation therapy .
3- Importance of prevention of infection
4- Importance of administration of medication .
5- Importance of not exposure to low oxygen environment like flying in unpressurized airplanes .
6- instruct parents about importance of follow up
Expected outcome :
Parents will understand of home care
5- Nursing diagnosis
High risk for complication related to chelation therapy and splenectomy